Product Description for NDUFS2
NDUFS2.
Presentation: Purified
Presentation: Purified
Properties for NDUFS2
| Product Category | Proteins & Growth Factors |
|---|---|
| Quantity | 20 µg |
| Synonyms | CI-49kD, Complex I-49kD, NADH dehydrogenase [ubiquinone] iron-sulfur protein 2, NADH-ubiquinone oxidoreductase 49 kDa subunit, mitochondrial |
| Presentation | Purified |
| Molecular weight | 46.5 kDa |
| Source | E. coli |
| Species (Protein) | Human |
| Shipping to | Worldwide |
| PDF datasheet | View Datasheet |
| Manufacturer | OriGene Technologies GmbH |
| Material safety datasheet | MSDS for Proteins (de) |
Datasheet Extract
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| Purity | > 80 % by SDS - PAGE |
| Background | NADH dehydrogenase [ubiquinone] iron-sulfur protein 2, mitochondrial isoform 1 precursor, also known as NDUFS2, is a 463 amino acid protein that is suggested to be required for catalytic activity. Defects in NDUFS2 are the cause of complex I mitochondrial respiratory chain deficiency, which is characterized by a variety of symptoms including liver failure, cardiomyopathy and neurodegeneration. Located in the mitochondrial inner membrane, mitochondrial complex I is the first and largest enzyme in the electron transport chain of oxidative phosphorylation. |
| Concentration | 0.25 mg/ml (determined by Bradford assay) |
| General Readings | Loeffen J., et al. (2001) Ann Neurol. 49:195-201. Procaccio V., et al. (1998) Genome. 9:482-484. |
| Storage | Store undiluted at 2-8°C for one week or (in aliquots) at -20°C to -80°C for longer. Avoid repeated freezing and thawing. Shelf life: one year from despatch. |
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